extramedullary hematopoiesis presenting as a right adrenal mass in a patient with beta thalassemia

Authors

hossein karami thalassemia research center, mazandaran university of medical sciences, sari, ir iran

mehrnoush kosaryan mazandaran university of medical sciences, sari, ir iran

mehrdad taghipour nephrology and urology research center, baqiyatallah university of medical sciences, tehran, ir iran.; nephrology and urology research center, baqiyatallah university of medical sciences, tehran, ir iran. tel: +98-2181262073, fax: +98-2181262073

rayka sharifian mazandaran university of medical sciences, sari, ir iran

abstract

introduction extramedullary hematopoiesis in the kidney and adrenal are rarely reported in medical literature and are usually found as incidentaloma. it usually occurs in patients with hematologic disorder such as thalassemia. case presentation the patient was a 23-year-old iranian man with beta thalassemia who was admitted with a suprarenal mass. adrenal mass was detected by ultrasonography and computed tomography. results of biochemical evaluations were insignificant. the patient underwent right adrenalectomy. gross and microscopic histopathologic examination demonstrated extramedullary hematopoiesis without any adrenal tissue. conclusions to the best of our knowledge, we document the first reported case of adrenal extramedullary hematopoiesis in iran, which seems to be rare and remarkable.

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Journal title:
nephro-urology monthly

جلد ۶، شماره ۵، صفحات ۰-۰

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